MOHAMMAD IMNUL ISLAM1, MANIK KUMAR TALUKDAR2, SHAHANA A RAHMAN3
Abstract
Background: The importance of Paediatric Rheumatic Diseases (PRDs) is increasing
globally day by day. These diseases are considered as important chronic cause of
childhood morbidity and disability. It is recognized that early recognition and diagnosis
as well as timely intervention can improve the outcome of PRDs.
Objective: To estimate the pattern of PRDs and to compare the profile of JIA with
other studies were done abroad.
Method: Retrospective study was done in the paediatric rheumatology clinic and in
patient department of Bangabandhu Sheikh Mujib Medical University (BSMMU) during
the study period from July 2007-December 2012. All the patients fulfilling the ILAR
classification criteria of Juvenile idiopathic arthritis (JIA), ACR classification criteria
of systemic lupus erythematosus ( SLE), PReS-EULAR-PRINTO classification criteria
of childhood vasculitis Bohan A, Peter JB Classification criteria for juvenile
dermatomyositis (JDM) and preliminary criteria for the classification of systemic
sclerosis (SS) were enrolled in this study.
Results: A total of 540 patients were enrolled. Highest number of patients had JIA
(77%), which was followed by SLE (10%). Among childhood vasculitis, Henoch
Shonlein purpura (HSP) was predominant (4.2%) followed by Polyarteritis nodosa
(1.9%) and Kawasaki Disease (0.6%). Juvenile dermatomiositis (JDM), systemic
sclerosis (SS) and rheumatic fever was also found in 1.6%, 1.3% and 3% cases
respectively. Polyarticular JIA was the commonest type (33 %) in this series, followed
by oligoarthritis, systemic onset and enthesitis related arthritis (ERA).
Conclusion: JIA was the commonest among the paediatric rheumatic diseases followed
by SLE and childhood vasculitis.
Keywords: PRDs, JIA, Vasculitis.