Congenital Acinar Dysplasia (CAD): Case Report of an Extremely Rare Cause of Pulmonary Hypoplasia

ABU FOIZ MOHAMMAD MIZANURRAHMAN1, AHMED AL ZOANI2, AAHMED AL AMERI3

Introduction
The primary function of lung is to accomplish exchange of oxygen & carbon dioxide to accommodate the need of aerobic cellular respiration . To accomplish this a large
thin alveolar capillary membrane is required.1Lung development takes place in 5(five) phases like 1.Embryonic phase 2.Pseudoglandular phase 3.Canalicular phase 4. Saccular phase and 5.Alveolar phase.1 CongenitalAcinar Dysplasia (CAD), an extremely rare form
of pulmonary hypoplasia, is a lethal condition characterized by arrest of lung  morphogenesis at the end of Pseudoglandular phase leading to non development of
acinar structure distal to terminal bronchiole resulting in absence of gas exchange betweenlungs and its circulationTreatment of this condition is limited to supportive
care.We are going to describe a case of lethal pulmonary hypoplasia caused by CAD.

 

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